Cystic fibrosis: current survival
Abstract
The aim of the multicentre study was to set up the national register and evaluate survival of patients with cystic fibrosis in Russia. Data were provided from the six special cystic fibrosis clinics and were used for national register. Six hundred thirty three patients (292 females and 341 males) were analysed.
One hundred eighty two patients were over 15 years (17%). In the beginning of the analysis, 107 patients (17%) were registered dead. Survival analysis has demonstrated that the mediana of expectant life is 25 years. It has demonstrated that significant difference exists in expectation of life between sexes (p=0.045). The mediana of expectant life in men is 29 years, whereas this parameter in women is 22 years. Our data have confirmed that cystic fibrosis is actual problem of pulmonology and isn’t only paediatrics problem any more.
About the Authors
E. L. Amelina
НИИ пульмонологии М3
Russian Federation
Russian Federation
A. V. Cherniak
НИИ пульмонологии М3
Russian Federation
Russian Federation
A. L. Cherniaev
НИИ пульмонологии М3
Russian Federation
Russian Federation
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Review
For citations:
Amelina E.L., Cherniak A.V., Cherniaev A.L. Cystic fibrosis: current survival. PULMONOLOGIYA. 2001;(3):61-64. (In Russ.)
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