Гиперчувствительный пневмонит: федеральные клинические рекомендации по диагностике и лечению

Гиперчувствительный пневмонит (ГП) представляет собой воспалительное и / или фиброзирующее заболевание легких, которое возникает в ответ на повторные ингаляции аэрозольных антигенов широкого спектра. Распространенность ГП составляет от 0,3 до 0,9 случая на 100 000 населения. Основу терапии ГП составляют глюкокортикостероиды, иммуносупрессоры, препараты с антифибротическими свойствами. Целевой аудиторией данных клинических рекомендаций являются врачи общей практики, терапевты, пульмонологи, патологоанатомы, рентгенологи и врачи по медицинской реабилитации. Методы. Каждый тезис-рекомендация по проведению диагностических и лечебных мероприятий оценивается по шкалам уровней достоверности доказательств от 1 до 5 и шкале оценки уровней убедительности рекомендаций по категориям А, В, С. Клинические рекомендации содержат также комментарии и разъяснения к указанным тезисам-рекомендациям, алгоритмы по диагностике и лечению идиопатического легочного фиброза, справочные материалы. Заключение. По данным представленных клинических рекомендаций освещаются современные сведения об этиологии и патогенезе, клинических проявлениях, диагностике и лечении ГП. Клинические рекомендации одобрены Научно-практическим советом Министерства здравоохранения Российской Федерации в 2023 г.

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