Ultrastructural ciliar lesions in primary ciliar dyskinesia
Abstract
Generally primary ciliar dyskinesia (PCD) is characterized by ultrastructural lesions of cilia. We performed electronic microscopic investigation of epithelium cilia in 99 patients in 1990–1999 years. PCD was found in 23 patients (13 males and 10 females). Ultrastructural lesions were provided more often by structure of internal and external denein ledges and radial spokes. A disorder of tubule’s disposition or losses of central tubule were noted extremely rarely. Information about frequency of ultrastructural ciliar lesions and their characterization will be useful for detection and differential diagnosis of primary and secondary disturbances.
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Review
For citations:
Ebsen M., Morgenrot K. Ultrastructural ciliar lesions in primary ciliar dyskinesia. PULMONOLOGIYA. 2001;(4):19-23. (In Russ.)
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