Bleeding from the gastrointestinal tract in cystic fibrosis patients with liver cirrhosis and portal hypertension
M. N. Sukhov,
N. I. Kapranov,
N. Yu. Kashirskaya,
A. V. Drozdov,
A. V. Kobiatsky,
S. Yu. Semykin,
T. Yu. Kapustina
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Abstract
From 455 Cystic Fibrosis patients 10.2% has liver cirrhosis. In Russia we were the first to introduce surgical means of treatment for portal hypertension in CF patients with liver cirrhosis. Sclerotherapy and portal venous shunting are used if variceal haemorrhage occurs. It was shown that all of them were palliative manipulations: portocaval shunts provided good control of portal hypertension but intensified liver failure, sclerotherapy did not prevent a recurrence of bleeding. In the future liver transplantation will be introduced for Cystic Fibrosis patients in Russia.
About the Authors
M. N. Sukhov
Отделение микрохирургии сосудов РДКБ; Отдел медицинской генетики РАМН
Russian Federation
Russian Federation
N. I. Kapranov
Отделение микрохирургии сосудов РДКБ; Отдел медицинской генетики РАМН
Russian Federation
Russian Federation
N. Yu. Kashirskaya
Отделение микрохирургии сосудов РДКБ; Отдел медицинской генетики РАМН
Russian Federation
Russian Federation
A. V. Drozdov
Отделение микрохирургии сосудов РДКБ; Отдел медицинской генетики РАМН
Russian Federation
Russian Federation
A. V. Kobiatsky
Отделение микрохирургии сосудов РДКБ; Отдел медицинской генетики РАМН
Russian Federation
Russian Federation
S. Yu. Semykin
Отделение микрохирургии сосудов РДКБ; Отдел медицинской генетики РАМН
Russian Federation
Russian Federation
T. Yu. Kapustina
Отделение микрохирургии сосудов РДКБ; Отдел медицинской генетики РАМН
Russian Federation
Russian Federation
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Review
For citations:
Sukhov M.N., Kapranov N.I., Kashirskaya N.Yu., Drozdov A.V., Kobiatsky A.V., Semykin S.Yu., Kapustina T.Yu. Bleeding from the gastrointestinal tract in cystic fibrosis patients with liver cirrhosis and portal hypertension. PULMONOLOGIYA. 2001;(3):50-53. (In Russ.)
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ISSN 0869-0189 (Print)
ISSN 2541-9617 (Online)
ISSN 2541-9617 (Online)
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