A role of Moscow regional register for management of cystic fibrosis patients
https://doi.org/10.18093/0869-0189-2013-0-2-27-32
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Abstract
Summary. This study was aimed at development of cystic fibrosis (CF) patient register for those living at Moscow and Moscow region. The CF patients living in Moscow region were found to have some clinical, genetic and bacteriological differences from CF patients living at the Western Europe. The median survival in 2003–2012 was 39.5 years. Aging of CF patients was associated to reduction in respiratory function, occurrence of more aggressive respiratory pathogens, increase in respiratory and gastrointestinal complication rate.
About the Authors
S. A. KrasovskyRussian Federation
E. L. Amelina
Russian Federation
A. V. Chernyak
Russian Federation
N. Yu. Kashirskaya
Russian Federation
V. S. Nikonova
Russian Federation
A. Yu. Voronkova
Russian Federation
E. I. Kondratyeva
Russian Federation
V. A. Samoilenko
Russian Federation
V. D. Sherman
Russian Federation
N. I. Kapranov
Russian Federation
M. V. Usacheva
Russian Federation
Zh. K. Naumenko
Russian Federation
Yu. V. Gorinova
Russian Federation
A. G. Chuchalin
Russian Federation
References
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Review
For citations:
Krasovsky S.A., Amelina E.L., Chernyak A.V., Kashirskaya N.Yu., Nikonova V.S., Voronkova A.Yu., Kondratyeva E.I., Samoilenko V.A., Sherman V.D., Kapranov N.I., Usacheva M.V., Naumenko Zh.K., Gorinova Yu.V., Chuchalin A.G. A role of Moscow regional register for management of cystic fibrosis patients. PULMONOLOGIYA. 2013;(2):27-32. (In Russ.) https://doi.org/10.18093/0869-0189-2013-0-2-27-32
ISSN 2541-9617 (Online)