Dynamic monitoring of a patient with idiopathic pulmonary haemosiderosis
https://doi.org/10.18093/0869-0189-2020-30-1-115-120
Abstract
Idiopathic pulmonary haemosiderosis (IPH) is one of the causes of alveolar hemorrhagic syndrome in adults; it is extremely rare. The results of clinical observation of a 42-year-old IPH patient with recurrent pulmonary hemorrhage in dynamics (within six months) are presented. The examination revealed anemia, bilateral infiltration process in the lungs, respiratory failure (SpO2 – 82% in the air). Differential diagnosis was made with autoimmune and non-immune causes of alveolar hemorrhagic syndrome. IPH confirmed by a percutaneous lung parenchyma biopsy. The patient has been successfully treated with systemic glucocorticosteroids in high doses.
About the Authors
E. V. Bolotova
Kuban State Medical University, Healthcare Ministry of Russia
Russian Federation
Russian Federation
Elena V. Bolotova, Doctor of Medicine, Professor, Department of Pulmonology, Faculty of Postgraduate Physician Training
ul. Sedina 4, Krasnodar, 350063
tel.: (961) 509-79-33
L. V. Shoulzhenko
Kuban State Medical University, Healthcare Ministry of Russia
Russian Federation
Russian Federation
Larisa V. Shul'zhenko, Doctor of Medicine, Professor, Head of Department of Pulmonology, Faculty of Postgraduate Physician Training
ul. Sedina 4, Krasnodar, 350063
tel.: (988) 244-82-49
E. A. Terman
Federal Research Institute and S.V. Ochapovskiy Territorial Teaching Hospital No.1
Russian Federation
Russian Federation
Evgenу A. Terman, a pathologist, Department of Pathology
ul. Pervogo Maya 167, Krasnodar, 360086
tel.: (918) 321-66-92
V. A. Porkhanov
Kuban State Medical University, Healthcare Ministry of Russia; Federal Research Institute and S.V. Ochapovskiy Territorial Teaching Hospital No.1
Russian Federation
Russian Federation
Vladimir A. Porkhanov, Doctor of Medicine, Professor, Academician of Russian Academy of Science, Chief Medical Officer, Federal Research Institute and S.V.Ochapovskiy Territorial Teaching Hospital No.1; Head of Department of Thoracic Surgery and Oncology, Kuban State Medical University, Healthcare Ministry of Russia
ul. Sedina 4, Krasnodar, 350063
ul. Pervogo Maya 167, Krasnodar, 360086
tel.: (861) 252-95-58
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Review
For citations:
Bolotova E.V., Shoulzhenko L.V., Terman E.A., Porkhanov V.A. Dynamic monitoring of a patient with idiopathic pulmonary haemosiderosis. PULMONOLOGIYA. 2020;30(1):115-120. (In Russ.) https://doi.org/10.18093/0869-0189-2020-30-1-115-120
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