The age-related assessment of pulmonary function in children with cystic fibrosis aged below 6 years
https://doi.org/10.18093/0869-0189-2019-29-6-739-744
Abstract
Cystic fibrosis (CF) is a severe hereditary disease associated with progressive impairment of respiratory organs. Pulmonary function test (PFT) in CF patients may be relevant for determination of therapy level and patient management strategy. However, PFT is particularly difficult in children aged below 6 years. Literature data concerning options for pulmonary function analysis in children aged below 6 years with CF for assessment of disease severity, progression and monitoring of treatment efficacy are provided in the article.
About the Authors
E. G. Furman
Federal State Budgetary Educational Institution of Higher Education "Perm State Medical University named after academician E.A.Wagner" of the Ministry of Health of the Russian Federation
Russian Federation
Russian Federation
Evgeniy G. Furman, Doctor of Medical Sciences, Professor, Head of the Department of the Intermediate Level and Hospital Pediatrics
ul. Petropavlovskaya 26, Perm', 614000, Russia
tel.: (342) 221-86-15
E. I. Kondrat'eva
Federal State Budgetary Scientific Institution "Medical and Genetic Scientific Center named after academician N.P.Bochkov"
Russian Federation
Russian Federation
Elena I. Kondrat'eva, Doctor of Medical Sciences, Professor, Head of the Scientific Clinical Department of Cystic Fibrosis, Head of the Scientific Clinical Department of Cystic Fibrosis
ul. Moskvorech'e 1, Moscow, 115522, Russia
tel.: (495) 111-85-80
A. V. Chernyak
Federal State Budgetary Institution "Scientific and Research Institute of Pulmonology" of the Federal Medical and Biological Agency
Russian Federation
Russian Federation
Aleksandr V. Chernyak, Candidate of Medical Sciences, Head of the Laboratory of Functional and Ultrasonic Examination Methods
SPIN-code: 9328-6440
Orekhovyy bul'var 28, Moscow, 115682, Russia
tel.: (495) 465-53-84
V. V. Shadrina
Federal State Budgetary Educational Institution of Higher Education "Perm State Medical University named after academician E.A.Wagner" of the Ministry of Health of the Russian Federation
Russian Federation
Russian Federation
Vera V. Shadrina, Candidate of Medical Sciences, Associate Professor of the Department of Intermediate Level and Hospital Pediatrics
ul. Petropavlovskaya 26, Perm', 614000, Russia
tel.: (342) 221-86-15
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For citations:
Furman E.G., Kondrat'eva E.I., Chernyak A.V., Shadrina V.V. The age-related assessment of pulmonary function in children with cystic fibrosis aged below 6 years. PULMONOLOGIYA. 2019;29(6):739-744. (In Russ.) https://doi.org/10.18093/0869-0189-2019-29-6-739-744
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