Hepatopulmonary syndrome in a woman with hepatic cyrrhosis
https://doi.org/10.18093/0869-0189-2019-29-4-493-498
Abstract
Hepatopulmonary syndrome (HPS) in a severe complication of advanced hepatic diseases. IHPS comprises the following triad of signs: 1) hepatic disease, 2) pulmonary vessels dilation, 3) hypoxemia without cardiorespiratory diseases. Clinical manifestations of HPS are cyanosis, finger clubbing, and platypnoea under the hepatic cyrrhosis. A clinical case of HPS in young woman with hepatic cyrrhosis is described in this article. HPS was resolved after the orthotopic liver transplantation.
About the Authors
A. G. Chuchalin
N.I.Pirogov Federal Russian National Research Medical University, Healthcare Ministry of Russia
Russian Federation
Russian Federation
Aleksandr G. Chuchalin, Doctor of Medicine, Professor, Academician of Russian Academy of Sciences, Head of Department of Hospital Internal Medicine. Pediatric Faculty, N.I.Pirogov Federal Russian National Research Medical University, Healthcare Ministry of Russia; Chairman of the Executive Board of Russian Respiratory Society
ul. Ostrovityanova 1, Moscow, 117997
N. G. Mirtskhulava
Krasnodar Territorial Teaching Hospital No.2, Healthcare Ministry of Krasnodar krai
Russian Federation
Russian Federation
Nona G. Mirtskhulava, Candidate of Medicine, pulmonologist, Head of Pulmonology Department
ul. Krasnykh Partizan 6/2, Krasnodar, 350012
D. V. Dremov
Krasnodar Territorial Teaching Hospital No.2, Healthcare Ministry of Krasnodar krai
Russian Federation
Russian Federation
Denis V. Dremov, pulmonologist, Pulmonology Department
ul. Krasnykh Partizan 6/2, Krasnodar, 350012
Yu. S. Panasenkova
Krasnodar Territorial Teaching Hospital No.2, Healthcare Ministry of Krasnodar krai
Russian Federation
Russian Federation
Yuliya S. Panasenkova, Candidate of Medicine, Pulmonology Department
ul. Krasnykh Partizan 6/2, Krasnodar, 350012
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Review
For citations:
Chuchalin A.G., Mirtskhulava N.G., Dremov D.V., Panasenkova Yu.S. Hepatopulmonary syndrome in a woman with hepatic cyrrhosis. PULMONOLOGIYA. 2019;29(4):493-498. (In Russ.) https://doi.org/10.18093/0869-0189-2019-29-4-493-498
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