pulmoПульмонологияPULMONOLOGIYA0869-01892541-9617Scientific and Practical Journal “PULMONOLOGIYA” LLC10.18093/0869-0189-2015-25-5-600-612pulmo-628Research ArticleОБЗОРЫREVIEWИдиопатический легочный фиброзIdiopathic pulmonary fibrosisАвдеевС. Н.AvdeevS. N.

д. м. н., профессор, руководитель клинического отдела ФГБУ «НИИ пульмонологии» ФМБА России, тел. / факс: (495) 4655264

MD, Professor, Head of Clinical Division, Federal Pulmonology Research Institute, Federal Medical and Biological Agency of Russia; tel. / fax: (495) 4655264

serg_avdeev@list.ruФГБУ «НИИ пульмонологии» ФМБА России: 105077, Москва, ул. 11&я Парковая, 32, корп. 4РоссияFederal Pulmonology Research Institute, Federal Medical and Biological Agency of Russia: 32, build. 4, 11th Parkovaya str., Moscow, 105077, RussiaRussian Federation201513012016255600612Copyright © Авдеев С.Н., 20162016Авдеев С.Н.Avdeev S.N.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://journal.pulmonology.ru/pulm/article/view/628

Идиопатический легочный фиброз (ИЛФ) встречается преимущественно у лиц среднего и пожилого возраста, являясь наиболее частым заболеванием из группы интерстициальных заболеваний легких. На протяжении последнего десятилетия произошли значительные изменения в подходах не только к диагностике, но и в определении ИЛФ. В данной статье представлены современные данные об эпидемиологии данного заболевания, приведены результаты новых исследований о патогенезе и основные подходы к диагностике заболевания. Кроме того, представлены новые данные о течении ИЛФ и наиболее часто встречающихся сопутствующих заболеваниях.

Idiopathic pulmonary fibrosis (IPF) is the most common interstitial lung disease which is prevalently diagnosed in older patients. The last decade, significant change took place not only in diagnostic approach to IPF, but also in definition of this disease. Recent data on epidemiology of IPF are described in this article, results of new studies on pathogenesis, natural course of IPF, comorbidity and principal approaches to diagnosis are discussed.

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The authors declare that there are no conflicts of interest present.