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<article article-type="research-article" dtd-version="1.3" xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance" xml:lang="ru"><front><journal-meta><journal-id journal-id-type="publisher-id">pulmo</journal-id><journal-title-group><journal-title xml:lang="ru">Пульмонология</journal-title><trans-title-group xml:lang="en"><trans-title>PULMONOLOGIYA</trans-title></trans-title-group></journal-title-group><issn pub-type="ppub">0869-0189</issn><issn pub-type="epub">2541-9617</issn><publisher><publisher-name>Scientific and Practical Journal “PULMONOLOGIYA” LLC</publisher-name></publisher></journal-meta><article-meta><article-id pub-id-type="doi">10.18093/0869-0189-2008-0-1-14-28</article-id><article-id custom-type="elpub" pub-id-type="custom">pulmo-1751</article-id><article-categories><subj-group subj-group-type="heading"><subject>Research Article</subject></subj-group><subj-group subj-group-type="section-heading" xml:lang="ru"><subject>КЛИНИЧЕСКИЕ РЕКОМЕНДАЦИИ</subject></subj-group><subj-group subj-group-type="section-heading" xml:lang="en"><subject>CLINICAL GUIDELINES</subject></subj-group></article-categories><title-group><article-title>Рекомендации по диагностике и ведению больных с дефицитом α1-антитрипсина Испанского общества пульмонологии и торакальной хирургии (SEPAR)</article-title><trans-title-group xml:lang="en"><trans-title>Guidelines for the diagnosis and management of α1-antitrypsin deficiency</trans-title></trans-title-group></title-group><contrib-group><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Видаль</surname><given-names>Р.</given-names></name><name name-style="western" xml:lang="en"><surname>Vidal</surname><given-names>R.</given-names></name></name-alternatives><bio xml:lang="ru"><p>отделение пульмонологии Университетской клиники Vall d’Herbon</p><p>Барселона</p></bio><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Бланко</surname><given-names>И.</given-names></name><name name-style="western" xml:lang="en"><surname>Blanco</surname><given-names>I.</given-names></name></name-alternatives><bio xml:lang="ru"><p>отделение пульмонологии клиники Valle de Nalуn</p><p>Астуриас</p></bio><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Касас</surname><given-names>Ф.</given-names></name><name name-style="western" xml:lang="en"><surname>Casas</surname><given-names>F.</given-names></name></name-alternatives><bio xml:lang="ru"><p>отделение пульмонологии клиники San Cecilio</p><p>Гранада</p></bio><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Жарди</surname><given-names>Р.</given-names></name><name name-style="western" xml:lang="en"><surname>Jardi</surname><given-names>R.</given-names></name></name-alternatives><bio xml:lang="ru"><p>отделение биохимии Университетской клиники Vall d’Herbon</p><p>Барселона</p></bio><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Миравитлес</surname><given-names>М.</given-names></name><name name-style="western" xml:lang="en"><surname>Miravitlles</surname><given-names>M.</given-names></name></name-alternatives><bio xml:lang="ru"><p>отделение пульмонологии клинического торакального института</p><p>Барселона</p></bio><xref ref-type="aff" rid="aff-1"/></contrib></contrib-group><aff-alternatives id="aff-1"><aff xml:lang="ru"><institution>Национальный регистрационный комитет дефицита α1-антитрипсина</institution><country>Испания</country></aff><aff xml:lang="en"><institution>National Alpha-1 Antitrypsin Registry Committee</institution><country>Spain</country></aff></aff-alternatives><pub-date pub-type="collection"><year>2008</year></pub-date><pub-date pub-type="epub"><day>28</day><month>02</month><year>2008</year></pub-date><volume>0</volume><issue>1</issue><fpage>14</fpage><lpage>28</lpage><permissions><copyright-statement>Copyright &amp;#x00A9; Видаль Р., Бланко И., Касас Ф., Жарди Р., Миравитлес М., 2008</copyright-statement><copyright-year>2008</copyright-year><copyright-holder xml:lang="ru">Видаль Р., Бланко И., Касас Ф., Жарди Р., Миравитлес М.</copyright-holder><copyright-holder xml:lang="en">Vidal R., Blanco I., Casas F., Jardi R., Miravitlles M.</copyright-holder><license xml:lang="ru" license-type="creative-commons-attribution" xlink:href="https://creativecommons.org/licenses/by/4.0/" xlink:type="simple"><license-p>Данная работа распространяется под лицензией Creative Commons Attribution 4.0.</license-p></license><license xml:lang="en" license-type="creative-commons-attribution" xlink:href="https://creativecommons.org/licenses/by/4.0/" xlink:type="simple"><license-p>This work is licensed under a Creative Commons Attribution 4.0 License.</license-p></license></permissions><self-uri xlink:href="https://journal.pulmonology.ru/pulm/article/view/1751">https://journal.pulmonology.ru/pulm/article/view/1751</self-uri><abstract><p>.</p></abstract><trans-abstract xml:lang="en"><p>.</p></trans-abstract></article-meta></front><back><ref-list><title>References</title><ref id="cit1"><label>1</label><citation-alternatives><mixed-citation xml:lang="ru">American Thoracic Society/European Respiratory Society Statement: standards for the diagnosis and management of individuals with alpha-antitrypsin deficiency. 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