pulmoПульмонологияPULMONOLOGIYA0869-01892541-9617Scientific and Practical Journal “PULMONOLOGIYA” LLC10.18093/0869-0189-2019-29-6-739-744pulmo-1259Research ArticleОБЗОРЫREVIEWВозрастные особенности оценки функции внешнего дыхания у детей c муковисцидозом моложе 6 летThe age-related assessment of pulmonary function in children with cystic fibrosis aged below 6 yearsФурманЕ. Г.FurmanE. G.

Фурман Евгений Григорьевич – д. м. н., профессор, заведующий кафедрой факультетской и госпитальной педиатрии

614000, Пермь, ул. Петропавловская, 26

тел.: (342) 221-86-15

Evgeniy G. Furman, Doctor of Medical Sciences, Professor, Head of the Department of the Intermediate Level and Hospital Pediatrics

ul. Petropavlovskaya 26, Perm', 614000, Russia

tel.: (342) 221-86-15

furman1@yandex.ruhttps://orcid.org/0000-0001-6395-0407КондратьеваЕ. И.Kondrat'evaE. I.

Кондратьева Елена Ивановна – д. м. н., профессор, заведующая научно-клиническим отделом муковисцидоза заведующая научно-клиническим отделом муковисцидоза

115522, Москва, ул. Москворечье, 1

тел.: (495) 111-85-80

Elena I. Kondrat'eva, Doctor of Medical Sciences, Professor, Head of the Scientific Clinical Department of Cystic Fibrosis, Head of the Scientific Clinical Department of Cystic Fibrosis

ul. Moskvorech'e 1, Moscow, 115522, Russia

tel.: (495) 111-85-80

elenafpk@mail.ruЧернякА. В.ChernyakA. V.

Черняк Александр Владимирович – к. м. н., заведующий лабораторией функциональных и ультразвуковых методов исследования

SPIN-код: 9328-6440

115682, Москва, Ореховый бульвар, 28

тел.: (495) 465-53-84

Aleksandr V. Chernyak, Candidate of Medical Sciences, Head of the Laboratory of Functional and Ultrasonic Examination Methods

SPIN-code: 9328-6440

Orekhovyy bul'var 28, Moscow, 115682, Russia

tel.: (495) 465-53-84

achi2000@mail.ruШадринаВ. В.ShadrinaV. V.

Шадрина Вера Владиславовна – к. м. н., доцент кафедры факультетской и госпитальной педиатрии

614000, Пермь, ул. Петропавловская, 26

тел.: (342) 221-86-15

Vera V. Shadrina, Candidate of Medical Sciences, Associate Professor of the Department of Intermediate Level and Hospital Pediatrics

ul. Petropavlovskaya 26, Perm', 614000, Russia

tel.: (342) 221-86-15

verashadrina@mail.ruФедеральное государственное бюджетное образовательное учреждение высшего образования «Пермский государственный медицинский университет имени академика Е.А. Вагнера» Министерства здравоохранения Российской ФедерацииРоссияFederal State Budgetary Educational Institution of Higher Education "Perm State Medical University named after academician E.A.Wagner" of the Ministry of Health of the Russian FederationRussian FederationФедеральное государственное бюджетное научное учреждение «Медико-генетический научный центр имени академика Н.П.Бочкова»РоссияFederal State Budgetary Scientific Institution "Medical and Genetic Scientific Center named after academician N.P.Bochkov"Russian FederationФедеральное государственное бюджетное учреждение «Научно-исследовательский институт пульмонологии» Федерального медико-биологического агентстваРоссияFederal State Budgetary Institution "Scientific and Research Institute of Pulmonology" of the Federal Medical and Biological AgencyRussian Federation201927022020296739744Copyright © Фурман Е.Г., Кондратьева Е.И., Черняк А.В., Шадрина В.В., 20202020Фурман Е.Г., Кондратьева Е.И., Черняк А.В., Шадрина В.В.Furman E.G., Kondrat'eva E.I., Chernyak A.V., Shadrina V.V.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://journal.pulmonology.ru/pulm/article/view/1259

Муковисцидоз (МВ) – тяжелое наследственное заболевание, при котором прогрессирует поражение органов дыхания. Исследование функции внешнего дыхания (ФВД) у больных МВ может быть значимо для определения объема терапии и тактики ведения пациентов. Однако у детей до 6-летнего возраста оценка ФВД особенно затруднена. В статье приводятся данные литературы по анализу возможностей исследования функции легких у больных МВ детей в возрасте до 6 лет для оценки тяжести заболевания, его прогрессирования и мониторинга эффективности лечения.

Cystic fibrosis (CF) is a severe hereditary disease associated with progressive impairment of respiratory organs. Pulmonary function test (PFT) in CF patients may be relevant for determination of therapy level and patient management strategy. However, PFT is particularly difficult in children aged below 6 years. Literature data concerning options for pulmonary function analysis in children aged below 6 years with CF for assessment of disease severity, progression and monitoring of treatment efficacy are provided in the article.

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The authors declare that there are no conflicts of interest present.